UtanoZvirwere uye Conditions

Ondine Syndrome: Zvinokonzera, tsananguro, kurapwa

Ondine chirwere - wakazonaka akadana vanachiremba nenguva dzirikure anombomira kufema, iyo inogona kuchengetwa zvose vacheche uye vakuru. Zvinenge sokuti, nei? Zvisinei, malfunctions kwakadaro reokisijeni kuti nhengo kungaita kwete chete kuti pave nezvirwere zvakasiyana-siyana zvomukati uye hurongwa, asiwo zvinouraya.

Nei achinzi?

zita raro, Ondine chirwere kwakakonzerwa mumwe mukuru ngano. Maererano naye, muridzi Ringshtetten Castle - Knight Guldbrandt - akarasika mune damn musango. Kubva vamwe rufu akamuponesa mubati wehove yekare, achipa pokugara mumba make. Zvaiva imomo kuti anokudzwa knight, uye kudanana usingafi njuzu Undine - old zvinosimudzira mwanasikana. Undine zvakare vaida Guldbrandt, uye akabvuma kuti ave mudzimai wake uye vobereka mwana wake. Usingafi njuzu pashure pokuberekwa mwanakomana wake dzikava chinhu unofa mukadzi munhuwo. Makore akawanda apfuura, makore rakaparadzwa Ondine vaimbova runako uye akatora rudo nomurume wake. Kamwe Ondine akaona murume wake ari maoko mumwe mudzimai wechidiki - Bertaldy. Chii chakazoitika, kuti ngano harinyatsotauri - kana Ondine rikanyuramo Danube pacharo, kana iri zvakamubatsira murume, akarasha pamawere. Asi Guldbrandta, nokukurumidza akasarudza kuroora vaduku Bertalde, vakamirira upenyu inotyisa: achioneka kwaari, mweya yose Ondine kutuka perfidious mutengesi, kumanikidza kuyeuka, kunyange usiku, sei kufema. Nokuti iye, hope yakava chinouraya, nokuti, akotsira, aisazova kukwanisa kudzora kufema kwako uye akafa.

Today Ondine chirwere - the kurongwa zita chemabhazi kufema mumwaka hope.

Chii chinoitika?

zita nesayenzi Official chirwere - ". hope kufema" It runoratidzwa kutyora mashandiro ari kufema muzinda paachabva pakurara, kufema. Kutaura pachavo, chirwere angabvuma achiri mucheche, uye chero nguva upenyu hwevanhu. Sowakajeka se nguva yokutanga munhu akamboona kutuka Ondine urwere, Wisniewski - yakakurumbira Polish munyori (muunganidzwa ngano pfupi "Tenzikadzi").

Kana murwere anoenda kunorara, ipapo, nokuti chero zvikonzero, muviri wake asingaiti aite otomatiki kushanda murau kufema, ndokusaka munhu haagoni kufema vakazvimiririra, uye sezvo zvakaguma pane Arikukachidzwa, kana sezvazvakanyorwa kunzi vanachiremba - disritmicheskaya hypoventilation. Panguva dzakadaro, yekudyidzana kwakaderedza padanho okisijeni kupinda muviri, nekuti iyo hwakaipa mashandiro vakawanda nenhengo dzawo, kusanganisira uropi.

Ndiani sei chirwere?

Kusiyana nezvimwe zvirwere kuti chokuita zvikurukuru vamwe vezera kana chechikadzi boka revanhu panguva chero zera vanogona kuratidza kutuka Ondine syndrome. In vakuru, chaizvoizvo kashoma chaizvo uye kunyanya akaona mu vacheche uye vana. Izvi zvinotsanangurwa nokuti pamberi Kakawanda kacho nyore havana kurarama kusvikira vakura, kukanganiswa kufema kukundikana vachiri vaduku. Mamwe mashoko chirwere kurara kufema vari zvakawanda mune vanhurume akura vanowanza kunge akapindira 40-fung mutsetse, uye mune zvisingawanzoitiki zviitiko - vakadzi.

Chii chinoitika kune muviri?

Sezvo sei Muviri womunhu kutuka Ondine chirwere - hope kufema? Chokutanga, pamwe vasanyanye padanho okisijeni muropa, kutambura kubva cardio-vascular hurongwa. Cardiac tsandanyama anotanga ndirambe dzinomutswa, midziyo rinooneka compressed, nokudaro kumutsa BP. In pauduku hwake, kana munhu achiri izere simba uye muviri hauna yakarohwa zvirwere zvakasiyana-siyana, izvozvo zvose anombozvitarisa. At kurei zera, kana muviri kare zvikuru "Worn" sezvinoita kunetseka usiku kungamutsawo nyore sitiroko kana mwoyo kurwisa, uye kunyange kurufu.

Mhando hope kufema

Ondine chirwere - iri kutyora kufema basa panguva hope kwete chete. Doctors kusiyanisa dzimwe mhando hope kufema:

  • peripheral (obstructive);
  • nechepakati;
  • yakavhenganiswa.

Peripheral kufema kunoratidzwa kakawanda, vanopfuura 15 nyaya paawa, anodzivira kufema basa, ane nguva kwazvo mumasekonzi 10. With kwakadai kufema wokufema rwokufamba anomiswa mu rokumusoro Airways, nokuda iyo mhepo haina inhaled mumapapu. Kazhinji, kutadza kufema kwakadaro kunoitika nokuda kutyora ndima tsinga nomunhu kuti pharyngeal uye kufema tsandanyama.

Central kufema kunoitika nokuti kuti Airways hamugamuchiri zvakafanira simba kupomba kubva nechepakati tsinga (CNS). Kukudziridza ezvinhu akadai, kazhinji zvichikonzerwa kwazvo Kumwe kuchinja kunotanga muuropi mamiriro, nokuda kunotevera kana chirwere.

Zviratidzo zviviri peripheral uye nechepakati apneas vakachengeta munyika dzinonzi yakavhenganiswa mhando, iyo kazhinji chirwere mu neonates uye vacheche.

zviratidzo

Somugumisiro zvinetso zvakadai hope kufema (kana peripheral, musimboti kana zvakavhenganiswa mhando), pane kugara vose vanoziva uye chavanoziva kudanwa, kuchinja hunhu kushanda kwomwoyo uye ropa midziyo. izvi zvose zvinotungamirira kukura zvinotevera zviratidzo:

  • zuva:

- yakakwirira nekuneta;

- Kugara kunzwa nokuneta uye nokushaya simba;

- mangwanani nomusoro;

- akaderedza kugona kuisa pfungwa uye ndangariro;

- Kusagadzikana mupfungwa.

  • usiku:

- nematambudziko akotsira uye kushaya hope;

- kakawanda nehope;

- vangadikitira;

- kuita weti kakawanda.

Kuwedzera kune zviratidzo izvi, sezvo kukuvara dzimwe nhengo uye hurongwa, kuchava nezviratidzo itsva nenyonganiso mabasa omuviri.

First Cause

Kusvikira yechipiri yezana remakore rapfuura, masayendisiti yaisanzwisisa chii chiri kukonzera kutuka Ondine urwere, ayo akakonzerwa haana zvakajeka uye zvisinganzwisisiki. Hapana aigona kupindura mubvunzo wokuti nei gwindiri vacheche uye vakomana, varume vakuru nevakadzi pakarepo akafa hope yake kufema kukundikana. Chete mangwanani 60-ies zviri XX remakore, vaongorori R. Mitchell uye George. Sevringausu zvakanzi vakawana kuti chirwere ichi inzira hope kufema. Izvi zvakawanikwa chakabatsira masayendisiti kuti murwere anenge warasikirwa otomatiki kudzora kufema somugumisiro zvikuru uropi. Uyewo varwere pamwe chirwere Ondine, mutengo murwere kuti kukotsira, sei kuongorora kufema basa, iye asingagoni, uye somugumisiro akatanga kumudzipa. Zvisinei, ongororo izvi havana kukwanisa kupindura mubvunzo chii chinoita zvirwere izvi munyika vanhuwo zvavo.

Chete ari XXI remakore vaongorori French vakakwanisa kumisa chikonzero chirwere ichi. Kuburikidza dzinotevedzana kuedza, masayendisiti akawana kuti kufema kukundikana kwemhuka ndiye anokonzera Thox2B Gene. Humwe mharidzo kuongorora vanhu vachitambura kubva chirwere Ondine, akasimbisa kuvapo chete Gene, uye vane. Chimwe chinokosha kuwanikwa akanga kuti majini mutation hauna nhaka uye kunoitika munguva embryo kukura.

kutuka Ondine urwere: Treatment

Kwenguva refu, kunze kubatana vanhu vanorwara usiku kudzora kufema muchina, anokwanisa kurwisa chirwere haana. Mumakore mashoma apfuura munyika dzakawanda dzokuEurope, akadai Sweden, Germany uye nevamwe, vava muchibereko muuropi, zvakananga ari phrenic etsinga, varwere pamwe chirwere Ondine chaiwo mano, iyo "zvinosanganisira" mweya painenge akamira. Maererano zvaanorumbidza varwere vakavhiyiwa, chero matambudziko pamwe kufema usiku, uye umo havachisiri kuwana masikati.

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