Lennox-Gastaut syndrome (pfari)

Lennox-Gastaut chirwere - mufananidzo nepfari (myoclonic-astatic). Kwakadaro zvirwere musimboti hunosanganisira mubatanidzwa tonic uye atonic nezvipusha, atypical Kusavapo nezvipusha, kunonoka kukura mupfungwa vacheche. Kokutanga chirwere kungazviratidza mune vana mumwe shanu, zvikurukuru vakomana.

kazhinji chirwere ichi achikura somugumisiro zvaitambidzwa uduku chetsinga zvirwere, uye inotanga pakarepo ichidonhedzera mwana. Kwapera nguva, pane kugwinha, nezvipusha, kuratidza anonoke mupfungwa kukura, uye kuderedzwa njere.

Zvishoma nezvishoma, pamwe kukura mwana, hunhu pfari siyana. Vachawira ne zvishomanana, kechipiri generalized, kurwisa dzakaoma kuti netsviyo.

Nokuda chii kunoratidzwa Lennox-Gastaut urwere

Kuti tinzwisise zvinokonzera chirwere ichi zvakaoma zvakakwana, asi kune zvevakomana anozivikanwa ndivo zvihombe.

• The anomaly uropi kukura.
• Zvakakomba Zvirwere (yomumuzongoza, encephalitis, rubella).
• Genetic pathological zvirwere uropi (CNS, metabolic zvirwere, tuberculous kuoma dzimwe nhengo dzomuviri).
• mwana akakuvara munguva ndima yokuberekwa Canal (kuberekwa asphyxia, magadzirira kubereka, etc.).
• CNS kukuvadzwa mune iri perinatal nguva, uyewo preterm kukurukura uye asphyxia.

zviratidzo PLGA

Lennox-Gastaut chirwere chinogona kuzivikanwa chinokosha chiratidzo - nokuti pfari. Vana vari chirwere "idiopathic pfari", rinorevawo siyana pamusoro nepfari (zviratidzo) :

• paroxysms ose mapopoma;
• atonic pfari;
• atypical tisipo;
• kukwana pfari;
• sternocleidomastoid chinyamunhari chinorwadza;
• myoclonic-astatic pfari;
• tonic pfari (kazhinji munguva nehope);
• TC generalized pfari.

Varwere vane chirwere pamusoro Lennox-Gastaut vanewo maitiro ezvinhu wekutsumwaira ine mvere kuchinja mu nepfari, retardation mupfungwa, zvishande uye unhu zvirwere.

Diagnosing kuti urwere LH

Pakarepo shure zviratidzo chirwere wokutanga hwobva kutsvaka kubatsirwa navanachiremba, dana amburenzi. Kazhinji, chirwere chirwere rinoitwa kushandisa ECG pakati kurwisa.

LH Syndrome Treatment

Lennox-Gastaut chirwere ari kurapwa uye zvomusejari nzira. Treatment pamwe mishonga pave zvakanaka hakuna kupfuura 20% nyaya. Mugore kuvhiya kurapwa nzira kuti kubvisa Madonhwe zvavhundutsa, zviri inobudirira kucheka corpus callosum (callosotomy). Uyewo, shandisa oparesheni kutungamirirwa kurudziro iri vagus etsinga uye kubviswa vascular anomera uye malformations.

Zvisinei, zvinofanira kucherechedzwa kuti pfari chinoratidza chirwere ichi nyore kubata; pakupedzisira vanogona kukonzera murwere kuti zvikuru munzanga uye mupfungwa. Zvinenge untreatable tonic nezvipusha, izvo zvinozoita kuti tikarega njere.