UtanoZvirwere uye Conditions

Huntington chirwere

chirwere Huntington haiwanzowaniki nhaka nyonganyonga. It kuzarurirwa munenge mumwe munhu muna gumi nezviviri. chirwere Huntington chinokurwadzai kunoramba kukanganisika tsinga. The guru kukundikana iri dzakaonekwa mbiri, iri pakadzika muuropi fuma, amazambiringa masero. Izvi goko uye caudate neerekitironi. Izvi nharaunda zvinobatanidzwa murau pamusoro zvemasanga zviito uri subconscious chechetere. Inokonzera chirwere Huntington haisiri pachena, asi masayendisiti kuramba kushanda panyaya iyi.

Zviratidzo chirwere kuitike, kazhinji pakati pemakore makumi matatu nemashanu kusvika makumi mashanu nemaviri. Huru kuratidzwa pematanho chirwere Huntington zvinosanganisira:

- mufambo zvirwere;

- kufambira mberi kuderera pfungwa basa kusvikira dementia.

Mukuwedzera, varege kuitika, uye zvimwe zviratidzo chokuita kusagadzikana tsinga.

Vazhinji varwere (anenge 90%) kubva nehosha yeHuntington kunoratidzwa involuntary spasmodic kufamba (chorea). Izvi kazhinji chiratidzo chokutanga.

Other kufamba zvirwere vanachiremba zvinosanganisira Rigidity, kana kuchinja tsandanyama matauriro, zvakaoma yokuzvidira kufamba uye matambudziko postural pamwe Kujeka emashoko mashoko (dysarthria), achinetseka pakuparadza (dysphagia), uye rwakakwana motokari runobva hunhu ziso.

Progressive zvishoma nezvishoma kuderera basa mupfungwa kuti anoenda chirwere Huntington, munogona pavanoparidza kukura chirwere chepfungwa. Varwere, kunyanya, vasingakwanisi pfungwa, kurasikirwa kwenguva refu uye pfupi-rokuti ndangariro, kukwanisa kunzwisisa uye kuwana kodzera matambudziko. Vamwe varwere, vaine kushatirwa, kuchinja mune zvepabonde, hukasha, kusakendenga, psychosis, kuora mwoyo.

Kana pane zviratidzo zvokurwara nokuda yakarurama zvokuongorora kunodiwa achisimbisa kuvapo urwere pakati nhoroondo yemhuri kwehama. Kushandisa nyanzvi kudzidza tsinga iri vatakuri zvemamiriro Gene kunoita kusarudza zvishomanana kuchinja nokukurumidza, kudzora kufamba nezviito refu isati nguva apo chirwere kuva raidaidzwa.

Laboratory kuongorora ropa kushandisa DNA ivhu akashandiswa Detective abnormalities mune mamwe mapoka. Idzi dzinosanganisira:

- varwere - Gene vatakuri;

- varwere uchapupu chirwere;

- vacheche mudumbu.

Zvisinei, zvinofanira kucherechedzwa kuti majini kutsvakurudza aigona kumutsa yakasimba zvakakwana mupfungwa uye kuisa pangozi mberi nzira pamuviri.

In muitiro diagnosing chinhu chinodiwa kuti asava zvimwe zvinokonzera chirwere kukura. Izvi zvinosanganisira, kunyanya vari kugamuchira zvimwe chikamu mishonga, sitiroko, kushungurudzwa pamusoro pakutsanangura nguva doro.

Nhasi chirwere haisi rinorapika. Zvisinei, shandisa kuchirapa matanho nechinangwa chokubvisa zviratidzo, nokuderedza zvikuru avo, uyewo pakupa mupfungwa uchenjerere varwere.

Pakati mishonga inogona kuderedza kukuvadza zviratidzo, phenothiazines kushandiswa. Ivo kudzora chorea. Treatment anosarudzwa zvakakwana nokungwarira, maererano zvinoitwa murwere kuitira kudzivisa marwadzo. Ramba kudzora Rigidity tsandanyama vanokwanisa zvimwe zvinodhaka - dopamine agonists. Zvisinei, tsika zvinoratidza kuti mune ichi, vari zvishoma inobudirira kupfuura Parkinson chirwere.

Kuderedza kuzvidya mwoyo, kushatirwa uye dzimwe zvinetso psycho-mupfungwa, varwere ndishandise physiotherapy.

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