Budd-Chiari urwere

Budd-Chiari chirwere kunoitika nokuda kunoramba obliteration (mukuvhara kana aienda) kuti lumen pamusoro tsinga zvikasabudiswa kupinda chiropa. Chiari aidavira kuti chikonzero chikuru - chikuru kuzvimba hepatic mutsinga. Asi pashure pacho akaziviswa mune zvimwe zviitiko, apo thrombosis pamusoro hepatic mutsinga akaderera vena cava.

The mabhuku anotsanangura anenge 200 zviitiko vatsvaire endoflebita mu hepatic mutsinga (chirwere , Budd-Chiari urwere).

With kukura thrombophlebitis arantsieva mutsinga dzinofamba nemukaka, izvo mainozonodira zvakananga kupinda kuruboshwe hepatic tsinga, achiine rukuvhute tsinga, uye ichi chirwere chinogona kuva muduku. The goko of hepatic mutsinga kana yomukati muduku vena Vienna (pedyo confluence chiropa) iri kukura, dzimwe nguva vakabatana ropa. izvi zvose kunokonzera okupedzisira kana aienda pamusoro lumen pamusoro tsinga, izvo zvinozoita hunokonzera kukura kurega kunotanga uye compression kuti chiropa masero.

Budd-Chiari chirwere hwapedyo uyewo mune dzimwe pathologies: nyanyisa neoplasms chiropa, rwatata, itsvo, nezvimwewo, vascular zvirwere generalized zvisikwa. Cirrhosis kunogonawo kukonzera kuti aienda pamusoro hepatic mutsinga. Chiari chirwere kungaita pane imwe localization Gunma echinococcosis, actinomycosis, abscesses uye zvichingodaro.

Akaora, Budd-Chiari chirwere kunoratidza zviratidzo huru chirwere, yakakonzera rimwe kuratidzwa ndiwo novimba ya occlusion pakati mutsinga. It anomira panze unopinza uye zvishoma nezvishoma chidzoke yacho syndrome.

Chenjera hepatic tsinga occlusion kunokonzera kamwe chimiro kurutsa, marwadzo zvakarurama repamusoro quadrant kana epigastrium nokuda chiropa, uyewo hyperextension Glisson Kamudzira, anovandudza ascites, panova yellowness.

Portal neBP hwapedyo panguva nemhaka nokukurumidza kuwedzera nevezera muna hepatic sinusoids uye mutsinga.

Ascites nechirwere ichi hachisi nomushonga diuretics, Urume runovaka chaizvo kukurumidza zvakare pashure paracentesis, dzimwe nguva vakapemberera kupinda ropa rake, anogona kuva hydrothorax. Kana anobatana thrombosis kuti anova ari muduku vena cava, ipapo ari kuzvimba panzvimbo dzapasi migumo, "Medusa musoro", uye nechiedza kumanikidzwa rinoshandisirwa payo, neropa ndokukwira.

With kukura hepatic tsinga occlusion zvachose anobatana mesenteric thrombosis, pane marwadzo uye manyoka, chetsinga yematambudziko kuonekwa nokuda kukuvara chiropa masero kuti zverufu mumazuva mashomanana.

Dzimwe nguva chirwere Budd - Chiari, pamwe rushoma kuvhara zviri lumen of tsinga kunogona kuitika sezvo chirwere chirwere kwenguva yakareba. With hunhu aibuda nguva yakadaro kunoitika rubatso kuparadzirwa: dilate zvachero ganda tsinga, portal neBP sokuti, uye ipapo anobatana uye esophageal varicose mutsinga.

Nokuti chirwere kunokosha pamberi kuderedzwa kumanikidzwa vari occlusal chiropa mutsinga uye mawa Zvakawanikwa portal kufurirwa, izvo dzakaonekwa pachishandiswa hepato- uye splenomanometrii nzira. Used retrograde rentgenogepatografiya umo kusiyana nevasori nezvevanakomana kupinda hepatic tsinga. Ultrassom Diagnostics pazvikanganiso zvakananga zviratidzo - kuri ropa clot ari mutsinga.

Pasina ruvara doplerrovskogo zvidzidzo zvinoratidza Budd-Chiari urwere mu:

• Kuvapo diffuse kuchinja pechiropa, hunhu zvikuru nuna chiropa kana fibrosis chiropa tishu,

• The mufananidzo hapana hepatic mutsinga Somuenzaniso, nokuda kwe lumen dzavo tinodzokorora positive vakawanda vari lumen,

• munhu aienda pamusoro muduku vena cava,

• zviratidzo portal BP, kana hosha kuripo.