Utano, Zvirwere uye Conditions
Aplasia (agenesis) Kidney: Zvinokonzera, zviratidzo uye kurapwa mamiriro
Pasina excretory hurongwa hazvibviri kufungidzira basa womunhu muviri. Mumwe yenhengo ayo neitsvo. Izvi aiwanzopiwa wokushanda Nhengo, chikuru basa riri imvura vachiwana uye mvura soluble okunze. Zvinonzi kubatanidzwawo zvakananga muviri uye mutemo asidhi-alkaline mwero. Muviri zvachose munhu utano pane neitsvo mbiri. At 2.5% kubva vachangoberekwa vari zvakaipa. Uye kunyange zvisingawanzoitiki, asi kuwana mwero itsvo.
Chii aplasia (agenesis) itsvo?
Zvinokonzera, zviratidzo uye kurapwa zvirwere zvisingawanzoitiki vakadaro ichakurukurwa pazasi. Chokutanga, munofanira kunzwisisa chii chinorehwa nemashoko aya.
In siyana dzokurapa mabhuku unogona kuwana musanganiswa pfungwa mbiri "aplasia" uye "agenesis". Pane musiyano pakati pavo? Agenesis - kushaya zvachose chimwe kana zviviri neitsvo mbiri. zvokurwara Izvi chokuziva. At nzvimbo asipo muviri hausi kunyange pedzidziso dzekutanga renal tishu. Aplasia - kutanga umo mune retroperitoneal mhango ndiyo chete beach kuti connective tishu. Mune mamwe manzwi, ndiye underdeveloped itsvo asingakwanisi kuita ayo ushande.
In kurapwa tsika, hazvina basa izvo chimiro chirwere inowanikwa muvana. Uye chokwadi, uye mune imwe nyaya, mumwe muviri yakazara vasipo. Single chirwere nhamba akapawo. Zvinozivikanwa kuti renal abnormalities pamusana anenge 7-11% vose pathologies ose genitourinary hurongwa.
nhoroondo mashoko
renal agenesis yave kuzivikanwa kuti vanhu kubva kare. chirwere ichi kunyange Aristotle vanotaurwa mumagwaro ake. Akataura kuti kana pane mhuka pasina mwoyo asingagoni, pasina itsvo kana chirwatata - zvachose. Mune Renaissance, dambudziko iri kufarira musayendisiti zveBelgium Andreas Vezaly. Muna 1928, Soviet chiremba Sokolov vakaisa kuziva kuwanda kwayo pakati yevagari. Kubvira ipapo, vatsvakurudzi dzinounzwa dzakawanda aplasia (agenesis), chimwe nechimwe chine zvayo kurapwa mufananidzo pachavo uye achifanotaura.
mhando agenesis
Kune classifications vanoverengeka chirwere. The huru kusiyanisa chirwere pamusoro nhamba miviri.
- Right madziro renal agenesis (bumbiro ICD-10 - Q60.0). Ichi chimiro chirwere anowanzodanwa chirwere vakadzi. Kazhinji kubva pakuberekwa rworudyi itsvo iri nyore. It riri pazasi kuruboshwe uye anonzi shoma Mobile. Kazhinji, vose mashandiro achipfeka aiwanzopiwa wokushanda nyere, uye munhu haasi kuona zvikuru kusanzwa.
- Kuruboshwe madziro itsvo agenesis. chimiro ichi zvirwere hariwanikwi uye anotakura zvakaoma zvakakwana. Kodzero itsvo iri shoma functionality. Hazvina dzakashandisa compensatory basa.
Tinofanira kufunga bilateral agenesis. Nokuti siyana ichi chirwere kunoratidzwa kusavapo vaviri mitumbi miviri. Under vana vake kashoma vapukunyuke. Pashure pokuzvarwa vakabva vanoda kuisirwa. Chii ane bilateral renal agenesis yekubvuma? ICD 10 inosanganisira zvokurwara pasi bumbiro Q60.1.
siyana aplasia
Ichi anomaly renal ndiyo chete angoramba achitaura. The pathological muitiro unogona kuparadzirwa vachingoshandisa kuruboshwe kana kurudyi muviri. Nokudaro itsvo fibrous zvinyama kazhinji kumiririrwa mu wokugaya chimiro, asi pasina chiuno, ducts uye glomeruli.
Zvinokonzera chirwere
Hakuna vabvumirana pamusoro zvinokonzera renal agenesis vachangoberekwa haako. Doctors vakaratidza akasiyana pfungwa maonero. Vamwe vanoona link pathologies ane majini kubatwa. Vamwe vanoramba chokwadi ichi.
kudzidza kwenguva refu kwechirwere chacho, uye ongororo dzakawanda vakabvumira kuziva zvinhu zvinoverengeka, kuvapo iyo kunowedzera ndingangokuvara parinowanika. Aplasia kana fetus itsvo agenesis zvinogoneka zvinotevera nyaya:
- Chirwere udhakwa, kushandiswa doro panguva yepamuviri.
- Chirwere cheshuga ari vanamai ramangwana.
- A nemavhairasi / zvirwere rokutanga trimester.
- Kushandiswa kusingadzoreki zvinodhaka mukadzi kweanodarika 9 months.
Itsvo dzinotanga kuumbika ari mudumbu kubva 5th vhiki hwake mudumbu. Izvi mberi yose pamuviri. Zvisinei, chinonyanya ngozi wa1 uye 2nd trimesters. Panguva ino, mukana wokuti kukura chirwere, akapa matambudziko vanoshorwa zvinhu, zviri kumusoro zvikuru.
The uchitikurudzira zvekuchipatara mufananidzo
Aplasia kana agenesis pamusoro itsvo ingava yakareba chaizvo haaratidzi pachayo nguva. Vamwe vanaamai panguva yepamuviri regai kuenda US, uye pashure pakuonekwa mucheche ndasiya Analyses. Somugumisiro, vanhu havana kutomboziva zviripo zvoutano. Adzidza risingafadzi zvokuongorora kwemakore. Kazhinji, panguva dzose bvunzo kuchikoro kana basa. Muchiitiko chino, mumwe itsvo utano Zvinotora pamusoro kusvika 75% of mashandiro ari asipo kana taita kushanda nenyere. Naizvozvo, munhu asingadi kunzwa chero kusanzwa.
Dzimwe nguva renal anomaly anotanga kuratidza mwana mumazuva okutanga muupenyu. Pakati huru zviratidzo zviri zvokurwara vanachiremba dzoga:
- siyana chiso kuremara (puffiness, rakafara uye sandara mhino);
- vakawanda wrinkles pamusoro muviri;
- vakombe dumbu;
- nzvimbo yakaderera nzeve;
- deformation repasi Mbabvu;
- zvaizopedza zvokudya zvimwe zvomukati.
Kana chirwere renal agenesis mwana, chirwere kazhinji pamwe zvemamiriro kugadzira nhengo dzokubereka nadzo. Somuenzaniso, vasikana kwakaratidza chine nyanga mbiri dumbu, kusangana nekutsi kwemukadzi Surgery. The Vakomana akawana kusavapo vas deferens. Mune ramangwana, matambudziko akadaro kunogona kuoma nokuda kusabetsera kana kunyange kushaya mbereko.
nzira nechirwere
Adult nguva dzose isa nechirwere "renal agenesis" urema. Zvisinei, unofanira kutanga kupfuura misoro kuzviongorora. Pamusangano chiremba anounganidza nhoroondo murwere zvokurapa, inodzidza ake enhaka kubatwa. zvimwe nzira tsvakurudzo kungadiwa kuzosimbisa rokutanga zvokuongorora:
- US.
- Urography pamwe Mukupesana mumiririri;
- Renal angiography;
- CT.
Kuti uone kusavapo kana itsvo fetus hypoplasia ivepo Ultrasound. Nechekare pakutanga rinovharidzira kudzidza, riri basa kuti 12-14 vhiki vakasuwa ari nyanzvi inogona kusimbisa zvokurwara. Pashure paizvozvo, mukadzi hazvo basa mamwe kuongorora kuti chokuita malformations.
kurapa kungaitwa pane kwakajairika
The chete chimiro chirwere, izvo chaizvoizvo rinomiririra ngozi kuupenyu - iri bilateral renal agenesis. Kazhinji zvibereko pamwe chirwere ichi kufa mudumbu kana pakuzvarwa achiri. Uyewo, mukana rufu mumazuva okutanga muupenyu shoma rakanyatsojeka kumusoro nokuda renal kukundikana.
Kuburikidza Kugadzirwa perinatal mushonga nhasi vane mukana kuponesa mwana zvokurwara uyu. Kuti aite izvi, muna rokutanga maawa pashure pokuberekwa kuvhiyiwa kuti ndinobvisa nhengo, uye ipapo kuti nguva hemodialysis. nzira iyi kurapa chirwere ariko uye rinoshandiswa tsika zvokurapa guru nzvimbo. Zvisinei, pakutanga zvinofanira kurongwa kutsanya differential chirwere uye vanodzinga mamwe malformations nezvezvimwe zvinetso zvedundira.
Yaitsigira divi renal agenesis ane zvakanaka fungidziro. Kana murwere kuti chirwere haisi kuoma nokuda zvisingafadzi zviratidzo, zvakakwana uchiongororwa zvegore uye kutora nemiedzo zvakakodzera. Zvinokoshawo kuti utarisire imwe itsvo utano. Detailed kurumbidza vanofanira kupa kurapa chiremba. Kazhinji, vanosanganisira zvaidiwa zvokudya kunze chakasimba uye wakawanda zvokudya, nokurega tsika dzakaipa.
Aplasia kwete zvikuru kurapwa. Zvisinei, unogona kuita pasina chokudzivirira vanorumbidza kusimbisa zvirwere. Unofanira kudya zvakanaka, dzivisa zvinotapukira uye nemavhairasi zvirwere. Zvinonzi Dzakamukurudzirawo kurega zvakakomba muviri.
In zvakakomba pathological muitiro kungada dialysis kana kunyange nhengo nokuisazve. Mune zvimwe zviitiko zvose, kurapa inofanira somunhu yakadekara hunhu chirwere uye uchitikurudzira kunotoda mufananidzo.
nzira kudzivirira
Aplasia uye agenesis itsvo Codes muna ICD-10 akasiyana. Zvisinei, vaviri zvirwere izvi zvinokonzera hanya pakati vanotarisira vabereki. Zvinoita kwakavatadzisa zvichiitika?
Kana iwe haabatanidzi nemagene kubatwa nezvirwere, kuti matanho ari nyore zvakakwana. Kunyange panguva kuronga rwakazara, amai vanepamuviri kutange kuongorora utano hwavo (vachidya zvakanaka, kusiya tsika dzakaipa, vanoita mitambo noitika). kurumbidza kwakadaro kunofanira kuteverwa pashure abudirire pamuviri mwana.
Kana usingagoni kudzivisa kukura ane zvokurwara, zvakakodzera kutora matanho ayo kubviswa. Kana pane bilateral agenesis zvakafanana, ichibata fetus kunonoka kukura, oligohydramnios. Kana kuziva miedzo anomalies pamberi kwevhiki 22 gestation inokurudzirwa kugumiswa kwayo pamusoro zvokurapa chikonzero. Kana mukadzi wake akaramba, akashandisa obstetric kuchinja nzira. Zvinokosha kucherechedza kuti pasina yaitsigira divi itsvo kunogona kuva upenyu huzere. Unofanira chete neapo kumbotambudzika chokudzivirira kunoonekwa nachiremba uye bvunzo.
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