UtanoZvirwere uye Conditions

Pancytopenia - chirwere pathological umo zvinoderedza iri achiparadzira neropa zvinhu zvose murwiyo. Zvinokonzera, zviratidzo, kurapwa

Chero Kugadzirwa hosha mumuviri kunokonzera kuchinja mukuita kubva peripheral ropa. Zvisinei, pane vakawanda pathologies iro kuchinja kwakadaro huru kunotoda chinhu. Pancytopenia - ndeimwe pathological dzinotsanagura ari hematopoietic gadziriro, iyo kunorondedzerwa so yakazvimirira chirwere, kana angava kuratidzwa nevamwe concomitant nosological.

General pfungwa

The chirwere haisi vakaderera, saka vanhu vakawanda havazivi kutanga kudaro. Pancytopenia - mumamiriro kushayiwa masero eropa, kukura iyo kunokonzerwa abnormalities marongerwo masero aizotangira ropa panguva padariro hematopoiesis. Kwakaderedza kwevari masero matsvuku eropa, ropa masero machena uye maplatelet nokuti kuti hunde masero havagoni zvakakwana kushanda.

Hosha ikabuda kaviri:

  • idiopathic, anokonzerwa zvemukati zvinhu;
  • yechipiri, izvo zviri kukonzerwa Kufurirwa nevamwe.

A pathological ezvinhu munenge 50% nyaya anovandudza autoimmune mhando. Kureva muviri anovarwira oga neropa masero ako, mistaking nokuti dzimwe nevamiririri. Idiopathic chimiro anogona ikamuka kuda kuti zvimwe zvekunze chinhu Inowedzera kukanganiswa mugumisiro.

Pancytopenia - chirwere chinogona nhaka, kukura panguva apo mwana ari mudumbu. Mwana anozvarwa kare nezvirwere ropa-Anoumba nhengo. Zvinogona vachiberekwa uye mwongo hypoplasia, saka kuti hurongwa havagoni kukurira mabasa avo.

The etiology chirwere uye ngozi zvinhu

Pakati kukonzera kukura chirwere vari nemagene kunotouraya, kushandisa zvinodhaka, radioactive kana chepfu Migumisiro-refu. Zvisinei, Idiopathic chimiro kunoratidzwa ndechokuti chikonzero anogona haangasimbiswi, kwaiva zviitiko chirwere pashure mukubereka vana.

Pave zvikonzero zvakakosha kuti zvakanaka mugumisiro. Achabvisa kwokunze pakufurira mu chirwere ichi - 50% wokurarama.

Kuwedzera zvikonzero pane zvakawanda zvinoita kuti kukura zvokurwara:

  • Shandai benzene kana Arsenic;
  • Fanconi kupererwa neropa;
  • ari nemavhairasi yezvakaita chirwere;
  • mishonga;
  • mishonga uye immunosuppressants;
  • autoimmune zvirwere zvakadai chinonzi systemic lupus erythematosus;
  • radiotherapy.

Fanconi kupererwa neropa - mumwe etiological zvinokonzera kuti pancytopenia. Anovandudza pamusoro pakanyorwa vachiberekwa anomalies anonzi ane autosomal recessive chirwere. Kupererwa neropa kunoratidzwa pamberi urema vari zvikamu mapuroteni anokonzera DNA kugadzira uye chromosome friability.

The kunotoda Mufananidzo chirwere

Pathological ezvinhu kunooneka pacharo muchimiro syndromes matatu. Mumwe nomumwe izvi maitiro zvinhu kuderedza uwandu imwe mhando masero eropa. Leukopenia kunoratidzwa mufananidzo rikwanise sepsis uye kwaita urikanwi-necrotic dzinotsanagura ganda uye mucous membranes.

Erythropenia uye nemuumbi zvinoderedza Chizenga kutsamwisa kukura zviratidzo kupererwa neropa. mamiriro ichi kunoratidzwa:

Varwere chokunyunyuta pamusoro kupfupika mweya uye mwoyo palpitations. Auscultation kuona rinyerere mwoyo pasi, systolic kutsutsumwa pamusoro pepasi mwoyo fungidziro, mubvumo pamusoro jugular tsinga. Kuwedzera murwere wacho nemamiriro kunokonzera zvachinja unonzi, electrocardiograph, iyo inoratidza kukura mwoyo kukundikana.

Thrombocytopenia kunoratidzwa kakawanda ropa (epistaxis, gastrointestinal, uterine), ropa matadza, chitarisiko petechiae uye hemorrhages paganda. Chenjera zviratidzo chirwere zvinochengetwa kwerinenge mwedzi uye kazhinji kurufu. Chirwere pancytopenia akabvumira nani. uye ane zvishoma raidudzwa zviratidzo

hosha anoonekwa kuti zvive zvakaoma zvikuru. Pancytopenia, izvo zvakaoma kunzwisisa zvakawanda zvakajairika kuti vanhu vakwegura, aine chimiro utachiona uye ropa.

chirwere matanho

nyaya yokutanga zvinoda zvivabatsire kune nyanzvi vaongo-, muunganidzwa nhoroondo uye upenyu murwere. Uyezve vakagadzwa CBC. Kana zviratidzo izvi zvinogona kufungisisa kukura pancytopenia uye kuitisa mberi chirwere matanho:

  • leukocytes <2 X 109 / L;
  • maplatelet <150 X 109 / L;
  • erythrocytes <3,5 X 109 / l.

Basa kudzidza ponji mumwongo iyo inorondedzera pamberi masero mwero uye myelokaryocytes. Hunodzorwa kuvapo abnormalities, kusanganisira mwongo hypoplasia. Also wakaitwa hemolytic ivhu.

pancytopenia kurapwa

Kuchirapa matanho kuvimba kunotoda nyaya, murwere ezvinhu uye etiological chinhu akakonzera chirwere. Zvinotevera kurapwa nzira inogona kushandiswa:

  • Ropa, chinonengaidza pakuenzanisa fomu zvinhu.
  • Transplantation kuti mwongo kana hunde masero. Kazhinji mabasa muvarwere vaduku uye pakati zera.
  • Kana autoimmune pancytopenia raitongwa immunosuppressant kushanda "Cytoxan", "Methylprednisolone," "Neoral", "Sandimun".
  • Zvinoreva anotokonya mumwongo kushanda - "Neupogen", "Neulasta", "Procrit", "Leukin".

zvinodhaka miti

The kurapa chirwere yakaoma kunosanganisira kushandisa yemakwenzi mushonga. The pamwero masero matsvuku eropa uye Chizenga vanogona kumutsirwa tichibatsirwa michero. Kusimbiswa teas dzinoitwa pachishandiswa padurunhuru, vatema currants, akasimuka hudyu, mastrawberry, michero, apirikoti. Nokuaina vapfumi turnips, gooseberries, Cherry uye mazambiringa, pokudya vasingadi chete yokufudza pakuenzanisa masero eropa, asi kusimbisa zvirwere.

Vanoverengeka chevarwere nzira chokubata pancytopenia unotora uchi. Zvinonzi pamwe anotevera zvinhu:

  • newaini tsvuku uye Aloe;
  • hadiyo;
  • oats;
  • ndimu, apricots yakaomeswa, akaomeswa, vanorichekerera uye fruit.

Batanidza zvikuru infusions uye decoctions yemakwati yorukato yorukato, Birch, uswa somuzivi, apila, voikukka, orkideat, apila, Buckwheat.

mhedziso

Pancytopenia - chirwere chakakomba, izvo anoenzanisa kuti chirwere chinouraya. Yakanaka Magumisiro pamusoro kwokuomerwa kurapwa zviratidzo, zvimiro uye zvokukura kukura umo kurapwa yakatanga. chirwere kwakadaro nyore kudzivirira pane mushonga.

The wegore dzokurapa kuzviongorora vagari kunoita kuti kuziva munhu pathological ezvinhu ari tanga. Zvikurukuru azvinoita mumarabhoritari kuongorora nzira.

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