UtanoZvirwere uye Conditions

Apert kuti chirwere - kunzwisisa nemagene chirwere

Apert kuti chirwere - isingawanzowanikwi chirwere, izvo kunooneka pacharo mune rimwe 20,000 vachangoberekwa. Ichi chisinganzwisisiki nemagene chirwere kuti kunoratidzwa nokuchinja Maumbirwe dehenya nokuda vakurumidze sinostozirovaniya (overgrowth) ari cranial sutures, uye mutezo abnormalities, kureva symmetric syndactyly maoko nemakumbo (yakakwana kana kukwana coalescence kuti dzakavakidzana minwe ruoko kana rutsoka).

Kokutanga zvokurwara ino vakaratidza chiremba French Apert muna 1906, ndichiona pfumbamwe vacheche vaifungidzirwa kuva majini chirwere. Apert akawana ayo maitiro features, uye akatsanangura urwere ichi.

Apert chirwere: zvinokonzera

Apert urwere, zvinokonzera izvo vachiri kuzivikanwa, zvinogona nhaka. Apert chirwere dzimwe nguva nemhaka yokuti panguva pamuviri amai vanepamuviri vakatambura zvirwere: rubella, yokuSpain, yomumuzongoza, tibhii , kana X-ray irradiation.

Apert chirwere: zvekuchipatara kuratidzwa

In varwere Apert urwere, anomalies yeDehenya uye zvimwe zviratidzo zviratidzo:

  • "Tower" dehenya - musoro kukura kunyanya kureba;
  • mukuru uye akakurumbira huma, guru nzeve;
  • flattened nasal zambuko;
  • Meso yakadzika-akaisa uye yakafara-akaisa;
  • nokuda kukura sandara zvigadziko pucheglazija;
  • Kazhinji mumukaha mukanwa - "mumukaha mukanwa";
  • Fusion of zvigunwe pamusoro maoko nemakumbo, munzvimbo mapfudzi, ivo emaoko;
  • Kugadzirwa kuomarara huru majoini;
  • kukakanganiswa mumuviri uye mupfungwa kukura;
  • dwarfism kazhinji wakacherechedza, kungava kurasikirwa kunzwa, horo imperforate, anomalies mu sechivako rwatata neitsvo;
  • Kumwe kuchinja kunotanga nameso chete cataract, strabismus, nystagmus, ptosis.

Chirwere pamusoro Apert chirwere pakutanga kunze pamusoro murwere chitarisiko. Next, murwere anoongororwa nokubatsira magene yokuedzwa.

Apert chirwere: pikicha murwere

Anounzwa munyaya mifananidzo ndiyo yakanakisisa kutaura pamusoro kwokunze chimiro murwere.

Apert urwere: Treatment

Apert chirwere marapiro aripo, asi kuvhiya rubatsiro runodiwa kuitira kudzivirira uye kururamiswa mumuviri urema uye retardation mupfungwa. Musimboti kwomudzimu mukuvhara coronary vazvo intracranial kumanikidzwa Tinozorodzwa aidawo uye orthodontic kuvhiya kupindira.

Nzira akavhiyiwa hereinafter inoitirwa kuumba zvigunwe pamusoro okumusoro migumo. Kazhinji pane dzinobatana pakati indekisi, pakati uye rin'i neminwe nokuda nyoro zvinyama uye kunyange pfupa. Vanachiremba kuvhiya pamusoro kuparadzana minwe kubva mumwe uye vawedzere functionality yavo.

Treatment rinoitwa chete kuburikidza ane Integrated kusvika. The chikwata VanaChiremba craniofacial kuvhiyiwa, neNeurosurgery, pfava, ophthalmologist, chiremba, chiremba wemazino, chiremba, orthodontist, vanopa rubatsiro mu nenguva nenzira.

The akavhiyiwa kuti upenyu nyore varwere Apert urwere, kuvabvumira kuzivisa mumuviri uye mupfungwa mano, wana hwandaiva chitarisiko, kuvandudza upenyu uye kuti vakaziva munzanga.

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