Zviratidzo uye vabatwe Landau-Kleffner urwere

Landau-Kleffner chirwere - inogona kuwanwa zvipusha aphasia vana. It kunoratidzwa kukanganisa kutaura chaitika. Muchiitiko chino, kutambudzika kwete kutsanangura zvinoumba kutaura (kurira nadzurudzo achishandisa mazino, rurimi, uye pahuro), uye kukwanisa nekutaura zviri phoneme nechepakati tsinga pamwero. Nenzira, zviri mune dzimwe nzvimbo dziri cerebral cortex.

Hosha rinowanikwa mune vana zvakakwana utano. Kutanga havachakwanisi ajairane zvokunze kwezvakatipoteredza, uye ipapo haagoni kuva anotaurisa, zvakajeka uye zvine musoro vataure zvavanofunga. Chokwadi kuti uropi mwana vari Kumwe kuchinja kunotanga, inoratidza eeg. The chirwere anorondedzerwa muna 1957 nemasayendisiti zviviri - Landau Kleffner. Naizvozvo, mazita avo uye kudana chirwere ichi.

The zvinokonzera chirwere

Zvinokonzera Landau-Kleffner chirwere haisi zvakazara kunorondedzerwa. Kunyange zvazvo dzimwe nguva, vanachiremba vanogona kuona kuti pave kukura chirwere. Pakutanga - ndiyo namahwindo Kukuvara musoro, rouropi, munhu parasitic chirwere anokonzerwa mazana kuti nyama yenguruve tapeworm - neurocysticercosis. The chikonzero chingava, uye autoimmune demyelinating zvirwere, umo kuparadzwa chena nyaya tsinga - myelin. Rinokonzera kukura chirwere vari kugonawo kuzvimba ari mudziyo pamadziro munzvimbo wouropi. Multiple kwokuonekwa zvirwere vakasonganira kushayikwa mitochondrial kufema kunzwisisa. Dzimwe nguva chikonzero yanyanya mutete cortex, zvichiguma mwana kusimukira kuti sei hemisphere.

The chirwere inogona fulminant chimiro. Ndizvo nezuro kukambaira-gore maviri akafamba, vakataura, uye aiva mwana gwindiri, uye iye zvino anomuka, vasingakwanisi kusunga, uye mashoko mashoma. Dzimwe nguva, zvirwere mberi zvishoma nezvishoma, muvhuruvhuru zvishoma nezvishoma anorasikirwa kukwanisa kwaro kutukana pakukurukurirana uye zvakakwana maonero chaicho.

Ndezvipi zviratidzo?

munhukadzi musayendisiti chirwere anorondedzerwa zvakadzama Alexandrov N. Sh Landau-Kleffner urwere, anoti, panewo nokuda anonzi uropi plasticity. Zvaiita sokuti "restructured" kuti nani kuita mabasa avo. Mukuita tishandurwe ichi uye anovandudza kwekanguva aphasia. Sezvakaita pamwe vawana chimiro, kukuvara uye zvirwere zvinokonzerwa kwakadai zvokurwara kunogona chirwere kushandisa eeg. Uyewo, "bhero wokutanga" vangava zvipusha nezvipusha, yakabuda panguva nembudzana. Vari 70% nyaya aine kutanga chirwere.

Around kota zvose nguva, murwere anorasikirwa kutaura mashandiro kwemwedzi. Asi vazhinji kurasikirwa kwayo kunoitika rakapotsa pakarepo. Dzimwe nguva mwana haagoni kutaura ruzha. Hafu varwere kuona maitiro asina kutsarukana. Operational kufunga hwaponeswa. With zera, kuti pfari zvachose. Full kana kukwana kupora kutaura mashandiro kuitika kwemakore 16.

Kuipa kutaura

Landau-Kleffner chirwere ari mwana rinotanga kurasikirwa mashandiro kutaura - ichi ndechimwe chikuru zviratidzo chirwere. It kunoratidzwa nemashoko kana auditory agnosia - vasingadzoreki maonero, izvo tichengetedze kuziva uye aikanganiswa. Muchiitiko chokutanga, murwere haakwanisi kutaura zvakanaka. In rechipiri - haagoni kuziva kujairana ruzha uye ruzha. Muchiitiko chino, zviri zvakajairika dzekukurira chirwere phonological audiogram.

Huru dambudziko riri chaiyo mumunda inzwi nehanya. Pasinei neizvi, chirwere kunooneka pachayo iri yakaoma mutauro kutora mudziyo. Vasingadzoreki kutaura playback anogona kuva akasiyana siyana kunzwisisa. Aphasia kwazvo simba mune vamwe varwere. Sezvo masayendisiti vanoti, akaoma zviitiko chirwere muna 6 varwere kubva 77. Kana mwana akaona zviduku kutyorwa, rinogona kuponesa kuverenga nekunyora. Language vachivavhiringidza kwakaratidzwa sezvinotevera: mwana Inovhiringidza tsamba uye sezvine zvakaipa kuvaka mitsara, haagoni zvine musoro kutaura pfungwa dzavo uye zvichingodaro.

pfari

Clinical pfari vari kuchengetwa 70-85% kuti zviitiko vawana Landau-Kleffner syndrome. Chirwere mune chetatu vana chinotanga kumbobatwa nepfari. Izvi - pakatanga chirwere. A nhamba wevarwere pakati kurwisa uye kutaura zvinetso zvinogona kutora makore akawanda. Pfari kazhinji wakaiswa nemakore kubvira 4 10 makore. vanachiremba vakawanda vanoti havana kuitika muupenyu akura. Kureva, pashure pemakore 16 pfari regai kuitika.

Muna 58% varwere wakaiswa kukwana pfari. Dzavo chinokonzera Uropi masero ari chaiyo munzvimbo imwe chepfungwa hemisphere. Pfari kuitika muna 39% vana, pfari vane kurasikirwa pfungwa - pa 16%. Vamwe varwere vakafumura myoclonic zvinetso kukanganisa tsandanyama chiso uye ziso maapuro. Muna 12% wevarwere netsviyo riri chinopfuudzwa panguva majini chechetere.

maitiro asina kutsarukana

Vane mamirire kwerinenge zvose varwere. 78% vana vaduku vane matambudziko zvounhu kana vari chirwere Landau-Kleffner syndrome. Vakuru havafaniri kushamiswa chokuti mwana wavo kamwe murunyararo uye rudo Reururai hasha. Hasha - mureza chiratidzo. Hasha dzinogona kuva chaizvo uye chin'a, kuti mwana haagoni mari kurarama nayo pasina muchipatara panzvimbo chepfungwa sangano. Vamwe, nekusiyana, Vachikwegura wakasuduruka payakakurudzirwa. Vanodzivisa boka revanhu kutambura kubva mwoyo uye nyanyisa pfungwa.

Vamwe vana sokuti chose matsi. Vamwe akaisa isiri zvokuongorora - autism. Zvechokwadi, vanachiremba vane dzimwe nguva zvakaoma kuziva chii chinokonzera vatorwa maitiro ane Landau-Kleffner syndrome. Handiti iye autistic maitiro dzinoratidzwa mananara dzakadai kutadza kuvaka musoro kukwana pfungwa, mashoko nyanyisa kudzokororwa chete zvirevo, mashoko. Simba Kuwanda hanya uye yakawedzera basa vakachengeta muna 80% wevarwere. Kunyange zvazvo matambudziko zvounhu vari yechipiri zviratidzo pazvinhu pakutaura matambudziko, zvimwe vana zvingakushamisa kujairika, musoro uye noshamisa siyana. Somuenzaniso, vanogona kupedza maawa tichidzokorora chete naJeremiya.

ano kurapa

At chiratidzo chirwere wokutanga zvakakodzera kutanga kurapwa kuti Landau-Kleffner syndrome. The kiriniki, umo iwe anoreva, uchakwanisa kupa chinetso dambudziko:

• Drug kosi;
• Kuvhiya.

Mukupera nyaya, murwere akavhura dehenya uye kubvisa zvipusha kukoshesa. Kuti aite izvi, akagura vamwe mapfupa uye zvakaoma goko wouropi. Pashure paizvozvo, vachena nyaya chiremba inoita incision. Vacharamba kudzivisa yatanga uye kupararira epileptogenic pulses. Ipapo reDhura mai uye mapfupa zviri kuiswa panzvimbo. The ronda sutured. Pashure 6-7 mavhiki pashure pokuvhiyiwa, mwana kubva kuchipatara vanogona kudzokera kumba. Pashure pokuvhiyiwa muvana pamwe Landau-Kleffner chirwere kuona kuvandudzika rezvedzidzo uye mafungiro mabasa.

Anti-kufenda

Mabatirwo Landau-Kleffner chirwere haisi nguva dzose zvinopa operative musiyano wezvinyorwa chete. Dzimwe nguva zvinobatsira kubvisa chirwere yezvokurapa mishonga. Inopa negashiro anticonvulsants. Zvinosuruvarisa, havafaniri nguva dzose kupa zvakanaka mugumisiro. Somuenzaniso, "carbamazepine", "Phenobarbital", "Phenytoin" kakawanda sashanda - aphasia anogona chete kuipa. Pfari Varwere achaiswa kudzokororwa aine kutsiva. Izvi ndezvechokwadi kunyanya varwere kakawanda pfari kana atypical kusavapo pfari.

Uyezve, vanachiremba kakawanda kuvakurudzira "Nicardipine". Zvinobatsira kuvhara karusiyamu makwara. Kubatsira ndiyo kwokubatsira intravenous gamma globulin. uye izvozvo zvakaratidza zvakakwana kunobudirira zvinodhaka "ethosuximide," "valproic asidhi". Help uye benzodiazepines, kunyanya "Clobazam" uye "Midazolam". Asi vanofanira kupiwa nomutsinga.

zvimwe zvinodhaka

Landau-Kleffner urwere, zviratidzo uye kurapwa izvo zvinorondedzerwa munyaya ino anopa negashiro "Diazepam" ndisati ndarara. mushonga uyu achipa nemigumisiro yakanaka. ARV ushandiswe kwenguva 6 mavhiki kudzivisa tachyphylaxis - nokukurumidza rutapudzo kushanda pamwe kushandisa zvinodhaka inodzokororwa. Ongororo dzakaratidza kuti zvingava anobatsira "levetiracetam". Zvinonzi zvakare kubatsira kwazvo pakurapa vaduku idiopathic zvatichiri nezvipusha, zvipusha zvemagetsi mamiriro hope, kudzvinyirira dzamarudzi Spike mafungu ake kunonoka chokutambudzika. Mukuwedzera, akabudirira pakurapa aphasia uye nezvipusha, mushonga "felbamate." Asi kana ukashandisa zvinobvira kuva akasiyana-siyana nemishonga, ramakagadzwa inonyanyoshandiswa akasangana aplastic kupererwa neropa uye chiropa dysfunction.

corticosteroids

In pakurapa Landau-Kleffner chirwere uye rubatsiro corticosteroids. "ACTH" zvikurukuru zvakanaka-nekusimba. It kunoderedza kuratidzwa zviratidzo vakatodzidza zvipusha aphasia, normalizes mamiriro ari eeg. Long-rokuti kurapa zvinodhaka izvi inokurudzirwa dzakawanda varwere. Zvisinei, ziva kuti haasi munhu wose rakakodzera hormone kurapwa kuita.

Kazhinji vanachiremba varayire steroids varwere. Somuenzaniso, "Prednisolone" chinotarisirwa nomutsinga pamusoro mitatu. The kurapa rinoshandiswa rekukangamwirwa induction. Zvakakosha kuyeuka kuti rutapudzo iri chipimo chemushonga pamusoro steroids runowanzotaurwa nezvarwo kuramba dzokororo chirwere zviratidzo. The zvachose nguva kosi hunogara kubva mwedzi mitanhatu kusvikira makore anoverengeka. Sezvineiwo, corticosteroid kurapa ane zvakawanda nemishonga akadai kufuta, BP, chirwere cheshuga, tsanga, itsvo kukundikana, kuora mwoyo, nemanic chirwere uye zvichingodaro. Mukuwedzera, havana pachii varwere vane matambudziko kutapata, sezvo ivo zvakare inoodza mwoyo naye. Vanewo contraindicated mune vanhu vane aseptic necrosis, tiibhii kana zvirwere vane chitarisiko wakatsamwisa zvinokosha mashandiro anoita roundworms.

Maonero vabereki

Special kunyatsotarisirwa kunodiwa kuti mwana ane chirwere Landau-Kleffner syndrome. Reviews nevabereki zvinoratidza kuti mwana vanofanira kutora nemakirasi chiremba wechikadzi achindidzidzisa kutaura, kutaura pathologists. Chiremba haagoni chidzosai kutaura chaitika. Asi Zvirongwa izvi kudzidzisa mafufu kuti kutsungirira, muuye naye basa, sangano. Vabereki vanoti vana kunze saka taurira munhu anticonvulsant akanaka uye antiepileptic mushonga unonzi "Keppra". We vanotiwo "Depakine," asi izvozvo kakawanda inokanganisa pamusoro rwatata, saka vamwe Achitaurazve Homeopathic kurapwa. Vanaamai vakawanda uye namadzibaba yakataurawo kuti nzira yakanakisisa pamwe chirwere - achikura mwana. Iye akura - iri zvishoma nezvishoma nani kutaura kwake. Uyezve, zera-mhanya kurwisa uye paroxysms.

mataridzikiro

Kana vanachiremba, naivowo kuramba kuongorora kuti Landau-Kleffner syndrome. Photo varwere mavhidhiyo Zvikamu dzavo, nhoroondo, akagumisa vanachiremba yakamanikana Profile - ichi zvose zviri chikamu tsvakurudzo. Vanachiremba vakaona kuti mishonga inoshanda nani ari chiitiko kuti mwana inopinda psychotherapy, kutaura makirasi. Full kuzoita kutukana anoitwa chaizvo hazviwanzoitiki. Kazhinji 2/3 Vana vakaponeswa zvakawanda kana zvishoma chakakomba chinetso chokutaura.