Chii Ollier chirwere. Ollier nehosha: kuongorora chirwere uye kurapwa

Iwe vaizofunga kuti dzenyu duku mwana makumbo kana maoko kukura zvishoma nezvishoma? Zvichida Ollier chirwere. Ihosha umo mune abnormalities pfupa Kugadzirwa marangwanda, kureva, ayo dysplasia. Other mazita vanotaurwa zvirwere - vakawanda chondromatosis mapfupa, yaitsigira divi kana chondromatosis diskhondroplaziya mapfupa. rokuremekedza ake chikuru chirwere chakanga nokuda wekuLyons chiremba Olier. The chirwere akaona uye anorondedzerwa kuburikidza nokushandisa maekisirei muna 1899.

Chii chirwere Ollier

chirwere ichi zvinoreva abnormalities ari mhou marangwanda, raiva zvirwere zvakawanda, kusanganisira kuzivikanwa nevakawanda moms vana hudyu dysplasia.

Kazhinji hosha kunooneka pauduku, nokuti chii akambopiwa akafunga kuti ichi chirwere chevana. Zvinonzi ikozvino akaratidza kuti zvokurwara aigona kuita debut wake vakuru (zvingaratidza kuitika kunyange zera siyana makore 20-40). Iri vachiberekwa abnormality, asi akawana nguva gare gare - mune muduku kana ari kuyaruka - kureva panguva ndichibvunza kukura, kana zvava pachena deformation mapfupa uye / kana zvemamiriro Kugadzirwa maoko nemakumbo.

chirwere Ollier ari metaphyses ekare mapfupa tubular nhengo dzake kuonekwa growths kuti shwashwa. Chirwere anovandudza kunyanya pfupa, shwashwa, uye mapfundo ramaoko nemakumbo, kunyanya tsoka uye nemaoko, uyewo vari chiuno, asi rinowanikwa mbabvu, sternum uye dehenya.

Growths kana enhondromy kuti chokunze paiva pfupa dzakatetepa uye haungatani kuputsika. Kutaura zvazviri, chinhu benign nebundu kuti anogona kuva nyanyisa (semuenzaniso, chondrosarcoma). Sezvineiwo, ichi zvinoitika chaizvo kashoma.

Pakuyaruka growths pakudzikamisa uye ne pfupa.

Saka, Ollier chirwere - rinorema nhaka chirwere, calcification of cartilaginous marangwanda umo uyewo kunoitika uye thickening metaphyses (mapfupa refu mumutsipa). Chikonzero parinowanika kuchiri kuzivikanwa. Mune zvimwe zviitiko, chinhu autosomal kuzivikanwa magene hunhu.

Zvakafanana diskhondroplaziey zvirwere hadziwanzowaniki syndromes maffucci uye Proteus. Pakutanga, kunze benign growths shwashwa uye skeletal deformities, ganda kuumbwa hemangioma - rima makwapa tsvuku mugari chimiro, rine tsinga. Dziri kusimukira yechipiri benign mapundu siyana nhengo dzomuviri.

Ndiani sei chirwere

Kare zvaifungwa kuti mapfupa chondromatosis isingawanzowanikwi. Asi ikozvino, kana X-ray Kuongorora rinoitwa nevakawanda zvakakwana, zvikazooneka kuti haisi husiri nyore kuwana. Kana makore 20 akapfuura, yakanga akarondedzerwa 30 nyaya kuti vari ikozvino kaviri sezvo vazhinji.

Kuti uone chaiyo kungoitika kazhinji hazviiti kana kubereka haasi pechidzidzo simba achishandisa maekisirei, kunyanya muduku uye fetus, apo, chaizvoizvo, pane Ollier chirwere. The chirwere, nenzira, vasikana kwakaratidza kusvika kaviri kakawanda kupfuura vakomana.

zviratidzo

Kwete kusuwa zviratidzo chirwere, vabereki vanofanira kuva vasingafariri kana mwana:

• kuramba kukura zvimwe zvikamu maoko nemakumbo / migumo;
• nemuumbi asymmetry uye vachigurisira mavari;
• akaona lameness;
• pane misalignment pakati chiuno;
• varipo curvature pakati pezvisungo zvenguvo valgus varus mhando kana.

All izvi zvinoita kuti tikwanise kufunga kuti mwana Ollier chirwere.

The chirwere haisi nguva dzose pakarepo pachena pakuzvarwa, asi pazera makore 1-4, uchaona kuti mwana nomumugwagwa kwaitora nguva pane zvaaitarisira, kuwedzera tsoka kana maoko. Ndiro huru chiratidzo chacho, risingagoni kungotariswa. Vamwe mwana ari kukura anowanzoita, pasinei akabatwa chirwere "Ollier chirwere."

Diskhondroplaziya kazhinji zvinokanganisa rimwe muzvidimbu Zvisinei pane zviitiko kukundwa vaviri. Kana hosha akabata pasi, mwana achava yakaderera kukura nokuda kupfupikisa yavo. Kunyanya kukakanganiswa zvakasimba mapfupa kana pathological muitiro akatanga mangwanani chaizvo. Deformation mberi inorwadza kunonoka mberi. Chokwadi, kugara kune chirwere, kunova mupfupi, mukobvu, kuchinja gait, lameness ari kuchengetwa. Pangava varus kana valgus wakarebesa pamusoro ibvi (nezvahwo - the proximal kuguma femur kana rutsoka), scoliosis pamusoro nomuzongoza. Muscle atrophy mune chirwere ichi hachisi chipo.

Big kuchinja pasi mumwe phalanx, metatarsal uye, mune zvimwe zviitiko, metacarpals. Ivo kutapudzwa, akawedzera, zveufende uye shwashwa ane enlightenments zhinji.

Ollier nehosha zvichida pakakuvara somugumisiro chirwere ivo vakava kururama pfupa. Zvisinei, mitswe kazhinji miganhu vashoma.

Comorbidities

Diskhondroplaziyu anogona kuenda maronda dzimwe nhengo, kunyange zvazvo zvirwere kufanana nounhu havasi nguva dzose. Zvikurukuru mune vasikana vaduku chete Ollier nehosha zvingaitika teratoma pakati ovary uye kwemakemikari anobudiswa zvinetso, kusanganisira zvakakomba, kusanganisira mangwanani chaizvo kumwedzi uye precocious kuyaruka wakakurumidza Ossificação em.

Zvisinei, kukura akadzokera chaiko nokubvisa ane ovary bundu.

Diagnostics

Kuziva chirwere Ollier kuti, zviri kutanga zvakafanira kuti rontgen. Panofanira kuva pfupa biopsy uye rinobva resonance kuri. Pamusoro kuonekwa pamusoro chirwere, varwere dzinoda kugara kunoonekwa nachiremba nachiremba, kana zvakakodzera, kuti nokukurumidza kuziva akaipa shanduko chondrosarcoma.

differential kuongorora chirwere

Differential chirwere kuti Ollier nechirwere, chokwadi, kwete zvakafanira pashure X-ray, nokuti mufananidzo kwazvo chaizvo chondromatosis. Zvisinei, mumwe nyaya iri nomumwe, asi kuva okurwadziwa zviratidzo dzinenge akadzokorora, saka vanachiremba vanofanira kutonga kubva wandei zvirwere zvakafanana.

Rontgen anobvisa atypical Chondrodystrophy, hemihypertrophy kana pfupa atrophy, rachitic deformation nevamwe zvirwere. Uyewo, nokuda maekisirei, Kwabviswa Recklinghausen chirwere, izvo kazhinji inogona vakavhiringidzika Ollier chirwere. The chikuru musimboti - vanofanira kuita chinhu X-ray rose marangwanda, pane chikamu.

kurapwa Guidelines

Diskhondroplaziya panguva, zvinosuruvarisa haana ouchenjeri nzira kurapwa. Kusiyana Somuenzaniso, zvirwere zvakadai hudyu dysplasia, chondromatosis kubatwa chete kuvhiya nokururamiswa deformation. Mune zvimwe zviitiko, kunoratidza hazvizivi hudyu kutsiviwa. Mamwe marapirwo kuti murwere vanofanira kugamuchira, - symptomatic uye aitsigira.

Kuvhiya kupindira zvinoratidzwa zvikurukuru vakuru, sezvo, maererano ano zvaanorumbidza, kana kuvhiya kuchikoro pazera kupindirana nemigumisiro vave nokugamuchira, izvo zvinoreva kuti pfungwa kuvhiya kurapwa chete kuumbwa panguva deformation, asi kwete simba. Zvisinei, mukunyombwa zvikuru zvinobvira kuvhiyiwa vana, kunyanya kana totaura minwe, ayo yekudyidzana yakavhiringidzwa pana Ollier chirwere.

The chirwere kunoda kuramba kwemajoini uye mapfupa: varwere kuratidzwa akapfeka vachibatsira shangu, kushandisa vachibatsira kufamba ndakaisa simbi mumakumbo nezvimwe mano kuti kugadzira majoini. Varwere vanofanira kuita akagadzirirwa zvakananga zvokurwara kurapwa ichi uye muviri nemitambo dzakaoma.

Yaibatsira sezvo jimunasitikisi uye kurovedza kunyatsonzwisisa simulators. Zvinobatsira kudzorera tsandanyama inzwi uye kusimbisa nemarunda.

mataridzikiro

Maererano nokutsvakurudza, kazhinji zviri pakuyaruka, shwashwa kuchatsiviwa pfupa (pamwe ndosaka ari vakura vanenge chirwere aonekwa chaizvo kashoma). Zvisinei, kuti anozivisa idukusa raduzhen mune vana vaduku: deformation, kunyange zvishoma nezvishoma, asi ari kufambira mberi. Zvanzi ngozi Ollier chirwere.

The chirwere kunoratidza pacharo saka nomumwe neimwe nyaya, kuti zvinonyatsorehwa fungidziro kwakaoma kuongorora zvisingarevi zvakawanda. Kana akawanda maronda zviri nani. kupfuura nyaya chete vemunyika nadzurudzo. Single deformation zvinotisvitsa kupfupikisa mumwe makumbo uye nokudaro, nokuda asymmetry dzavo, kunyanya kana totaura vana vaduku. Uye hazvibviri kugadzira. Uyewo mukutanga kukura kenza kunowedzera mikana deformities siyana nemimwe.

Kushandurwa kupinda chondrosarcoma

Pasinei chokwadi kuti akaipa kwokushanduka maonero - chondrosarcoma - zvikasaitika kazhinji, asi pane mukana yokuva nekenza. Kunyanya ichi zvinoitika kuyaruka, kunyange zvazvo nhamba kutsvakurudza ano kunoratidza kuti zvinogona kuitika zvikuru gare gare. Nokuda kwechikonzero ichi, varwere vari yakarumbidza diskhondroplaziey dzose yokubvunza chiremba uye zvokurapa bvunzo.