UtanoZvirwere uye Conditions

Hypertelorism - chii ichi? Zvinokonzera uye zviratidzo

Hypertelorism - izwi, naro chinorehwa munhu zvokurwara chemafuta akawandisa kuwedzera kure pakati vaviri aiwanzopiwa wokushanda nhengo. Muzviitiko zvizhinji nechirwere ocular hypertelorism, asi vamwe kuchinja pathological mune ano okurapa. Izvi ndizvo zvatinofanira tsanangura gare gare munyaya ino.

Hypertelorism - chii ichi?

Ichi ndechimwe chaizvo mune zvokurapa zvinyorwa. Hypertelorism - ndiko, Sezvambotaurwa, pane zvokurwara icho pamwe nokuwedzera kure pakati vaviri aiwanzopiwa wokushanda nhengo. Zvinofanira kucherechedzwa kuti tsanangudzo akatanga kushandiswa kudaro kare - kokutanga mumabhuku yepamutemo, izvozvo akaonekwa 1924.

Somuenzaniso, mune zvokurapa aizivikanwa somunhu zvokurwara akadaro hypertelorism minyatso. Muchiitiko chino, kutyorwa vanonzi munyatso Index - indekisi, zvakatemwa kubudikidza reshiyo pakati sekamufarenzi pechipfuva panguva ufanane munyatso uye kure pakati pavo. Zvokurwara haisi yakazvimirira uye kazhinji anova pamusoro pakanyorwa vachiberekwa malformations, akadai Apert urwere, Edwards 'chirwere.

Asi rakajairika orbital hypertelorism - chirwere iyo pane zvemamiriro nokuwedzera kure pakati ziso nezvigadziko. mamiriro akadaro chokuziva - zvichinzi chirwere mumazuva okutanga pashure pokuberekwa.

Ndezvipi zvinokonzera chirwere

Hypertelorism ziso - vachiberekwa nyonganyonga, iyo kazhinji chokuita zvakasiyana nemagene zvirwere. Somuenzaniso, zvakare zvikuru munzvimbo dzokuzororera dzaiva ziso nezvigadziko zviri kuchengetwa vana nefrofibromatozom, Apert urwere, chirwere cheDown syndrome, tositi, Edwards uye zvimwe zvirwere zviri pamwe vakawanda malformations ari mudumbu. Nokuda kwezvikonzero zvakafanana rakananga zvinosanganisira abnormalities siyana muuropi mamiriro kana dehenya - ndiyo kuvapo namamota, zvakare kukurumidza nokuporesa dehenya zvikamu, dzechimwe uropi herniation uye crevices.

Zvechokwadi, zvinokwanisika kuziva zvimwe zvinokonzera njodzi kuti zvinogona kuvhiringa zvakajairika pamuviri kukura , kana rinokonzera iripo fetus nemagene abnormalities. Saka, zvakaipa kukanganisa mwana nemamiriro kukanganiswa chirwere Kutamiswa amai pavanenge vakazvitakura, uyewo kupinda muviri muchetura, kusanganisira zvinodhaka inorema, yakakwirira mishonga doro, mishonga uye zvichingodaro. D.

Hypertelorism: Mufananidzo uye vakabatana zviratidzo

Zvinonzi hypertelorism ane zvakasiyana dhigirii - vamwe varwere ziso chete zvishoma misha, apo vamwe vari paupamhi kunze uye chiremba wako tingaona chakaremara pashure yokutanga Kutarira mwana. vana ava vane maitiro chaizvo chiso zvechiratidzo chacho:

  • kure Pathologically guru pakati zviso zvigadziko yomukati.
  • Kazhinji deformation palpebral Kunetsana aona - vanogona kuva mugari chimiro, kana kuva asymmetrical kujekesa zvikuru.
  • Panewo maitiro nemamiriro mhino - musana wake sandara uye yakafara mhino zambuko.
  • Kazhinji hypertelorism muvana nechirwere strabismus, siyana pamusoro kutadza kuona zvakanaka, ari deformation ari optic etsinga, kuti dambudziko munhuhwi.

Sezvineiwo, apa nemagene zviratidzo mamirire kwete chete kutyora pamberi nemamiriro dehenya. Kazhinji, vana vane rutsoka deformities, zvemamiriro Kugadzirwa shaya, havachanyatsogoni rezvedzidzo kukura.

chirwere nzira

Zvechokwadi, muchiitiko ichi, zvakakosha chaizvo rokuongorora nemazvo, nokuti unofanira kuona kuvapo imwe nemagene chirwere. Doctor anoti ichi interorbit okruzhnostnoy-indekisi, zvakatemwa kubudikidza kugovera akayera musoro sekamufarenzi kune chinhambwe pakati yomukati makona meso slits, uye kunoguma nhamba zvikawanda ne 100. The zvokurwara kazhinji akati panyaya apo indekisi kwazvo 6.8 .

Uyezve kuitwa anamnesis vabereki uye magene tsvakurudzo. Uyewo, iva nechokwadi mwana wenyu ari ushandiswe rinobva resonance kana computed tomography musoro - nzira iyi inogona kuona pfupa abnormalities uye kuvapo namamota muuropi.

kurapwa chirwere

Kana isu kutaura hypertelorism, ipapo marapiro kunodiwa chete chiitiko kuti pane ngozi mapazi zvaakaratidzwa uye tsinga harinzwi. Muchiitiko ichi Zvinokurudzirwa kuvhiyiwa. Munguva nzira, chiremba anoita epurasitiki dehenya. Asi chokwadi, kusarudza mubate vakadai kuvhiyiwa kunoda nyanzvi kuteerera zvinhu zvakawanda, kusanganisira mwana wacho mamiriro uye kuvapo comorbidities. Kuvhiya ari raiwanzoitwa pamberi murwere makore maviri - ndiyo nguva iyo oparesheni anopa zvikuru Zvakanyanya Kunaka Panguva Yepamuviri zvabuda.

Kana systemic kunorapwa, izvozvo inoendeswa rakasungwa zvikuru chirwere. Kubva ichi uye zvinoenderana zvokurapa kurapa.

Kudzivirira zvirwere uye fungidziro wevarwere

Hypertelorism - asi, chinhu aesthetic kuremara. Njodzi zvinosanganisira syndromes uye nezvirwere izvo pamwe ne chirwere. Saka, ndiko kuremara pacharo hausi kukanganisa upenyu mwana. The chete kunze vaya zviitiko apo ziso nezvigadziko degeneration kunokanganisa murwere chiratidzo.

Panyaya kudzivirira, asi urombo chaizvo nzira yokudzivirirwa kurondedzerwa ptologii hakuna. Kuderedza ngozi intrauterine zvirwere, panguva yepamuviri vanofanira kunyatsoongorora kuongorora utano, mudye zvakanaka, kusvuta, doro, mishonga uye zvinodhaka nengozi.

Achironga pamuviri uye inofanira kubatwa nenzira uye kwete kusiya vakaronga zano rimwe geneticist. Zvimwe zvirwere majini inogona chirwere kunyange utero. A majini kudzidza panguva yekuronga pamuviri kukubatsira kuona mukana wokuti mwana yakatsauka.

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