Utano, Zvirwere uye Conditions
Darier nechirwere: zvinokonzera, zviratidzo, kurapwa
Vazhinji vanhu chaiyo yakatofanana vabereki vavo. Mumwe anopiwa zvitema meso papa, mumwe - mai chic nebvudzi. Chokwadi, dzimwe nguva vakutarisire. Zvisinei, isu tose vachikura zvinonakidza nemigumisiro kugadzira majini dzepedyo dzedu. Kakawanda, nameso hombe, rakamonana bvudzi uye nemakumbo refu, vabereki vanopa vana vavo kuva zvirwere zvakasiyana. Vanoita izvi kwete chinangwa, kunyange pasina yako mvumo. Zvokurwara kurege kuitika muupenyu hwose, asi kakawanda zvakasiyana. Munhu anova mubatwa zvirwere mhuri uye zvirwere. Mumwe "zvipo" izvi ndizvo Darier chirwere. Chii? Chii chinokonzera zvokurwara ichi?
Vhuṱanzi
Under chirwere Darier zvinoreva nhaka dermatosis akaratidza mapundu muchimiro nodules shava kana shava. Ndivo cône serin'i akafukidza gobvu crusts. Nodules vemunyika pamusoro muviri pazvirugu kuuya pamwe uye dzinoumba ronda nyoro. Zvichienderana nzvimbo maronda avo pakuonekwa, chirwere Darier kuti rakakamurwa siyana zvina:
- Vemunyika. Dzinoratidzwa Linear nokurongwa nzvimbo iyo kufukidza chete munzvimbo shoma mumuviri.
- Classical. Upundu runonyanya vemunyika mumusoro, chipfuva uye nzeve.
- Isolated. Pamwe mureza nodules kuonekwa polyhedral papules chakatodzana nemburwa. Kazhinji, vari seri maoko netsoka.
- Vesicular-bullous. Ichi chimiro chirwere hariwanikwi chaizvo. It kunoratidzwa vakawanda maronda pamwe segirazi chakavanzika. Vanoonekwa kudivi pamutsipa, munzvimbo huru ganda pazvirugu.
Primary maronda papules vari panoonekwa Varwere pakati pemakore masere kusvika nemashanu. Adult chirwere parinouya kashoma.
The zvinokonzera chirwere
The chikuru chinokonzera chirwere ichi ndicho pamberi zvemamiriro Gene, uye chikuru ngozi - nhaka kubatwa. Somugumisiro, vhitamini A haisi zvakazara woga nomuviri, basa dzimwe makemikari zinc tigutsikane ari Epiderme e ipfupi. Mhedzisiro pathological azvaiitwa ari kutyora mashandiro ganda keratinization.
Kana amai kana baba vari vatakuri zvemamiriro Gene muna 50% nyaya, chiedza anooneka mwana chirwere kuti "Darier chirwere." Zvisinei, kana varwere vabereki vakaberekerwa mwana zvachose utano, zvokurwara ichi hazvisi kunetsa vana vake vomunguva yemberi. The chirwere haisi pachishandiswa kuenda neherikoputa mumate kana zvepabonde.
zvekuchipatara mufananidzo
The pathological kwacho kunotanga chitarisiko sandarara follicular nodules, ayo zvimwe aizivikanwa papules. saizi kwavo dzinosiyana 1 kusvika 3 mm. Papules yakafukidzwa yakasimba goko dzebhurauni ruvara. Pasi payo pane dzegirini mu chimiro fanera. Nodules chiri panzvimbo miromo bvudzi follicles, izvo dzimwe nguva kunoita kuti pave nomumwe chirwere - folliculitis. Saka, asati atanga kurapwa zvakakodzera kuitisa differential kuongorora chirwere.
Kwemakomo vanosarudzirwa symmetrically ichitora subclavian nharaunda uye flexor hukawanika ari mapfundo. Mumusoro papule nowenyika warty scaly plaques pamwe crusts. Mushure Kubviswa ravo munzvimbo maronda kuonekwa foci kuti alopecia. Sezvo chirwere mberi kune rashes zvitsva nezvitsaru dzinobatana mugomba chete nzvimbo.
Medical ongororo
Chirwere chirwere anobva kumwe mufananidzo uye kwakakwana nhoroondo dzokurapa zvomurwere. Panguva yokuongorora, chiremba anoongorora zviratidzo chirwere, zvapfuura zviitiko rashes pakati pedyo nehama. Kuzosimbisa chirwere iri hurukuro histological kuongorora ganda biopsy. The differential chirwere rinoitwa pamwe rwapedyo pemphigus, papillomatosis uye seborrheic dermatitis.
kurapa misimboti
Treatment pamwe chirwere ichi raiwanzoitwa pamusoro outpatient hwaro. Panguva exacerbation of pathological muitiro rinowanika kana yakakura maronda murwere kunoda muchipatara vari kuchipatara dermatological.
Murwere ane symptomatic kurapa. Varwere All asingasiyi basa vhitamini A muchimiro nomumukanwa kana intramuscular jekiseni. Chipimo chemushonga rinowanikwa nomumwe, kufungisisa murwere zera. Yawapiwa rinowanzova 3 months, ipapo kuregawo uye kudzokorora kurapwa.
A yakanaka mugumisiro pamwe Darier chirwere vanopa sefuro dzokugezera akabatana mafomu keratolytic mafuta. In pamberi maronda makuru, kuvhiya kupindira kana electrocoagulation. Apo chirwere Darier iri pamwe kuwedzera imwe noutachiona, mushonga unorwisa iri ushandiswe.
Kufembera uye kudzivirira
Maperembudzi wakapiwa chete nhaka. Ndokusaka sechinhu chikuru nyanzvi kudzivirira dzinokurudzira kubvunza ane geneticist kune vakaroorana kuronga iri pedo nguva yokubereka mwana. Izvi ndezvechokwadi kunyanya vabereki, uyo ari mhuri watopiwa chirwere Darier chirwere.
Kurapwa pamusoro apa, kazhinji zvinoratidza migumisiro yakanaka. Varwere vakawanda anogona kuzadzisa kuregererwa anomira kwemakore mashoma. Zvisinei, mumwe haafaniri kutarisira kunaya zvakakwana.
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