UtanoZvirwere uye Conditions

Wegener kwakaita granulomatosis - Zvinokonzera, zviratidzo, kurapwa.

Wegener kuti granulomatosis - ndiyo imwe autoimmune chirwere hwokuratidza kuzvimba arteries diki uye mutsinga. Kazhinji mashoko anorwadza tsinga vachigovera ropa sinuses, yemapapu uye itsvo munyama asi, mukuwedzera, pane rushoma zvitarisiko ari chiitiko chinobata chete mumwe zvikamu izvi. With zvakawanda granulomatosis dzinenge nguva dzose vanoshamiswa zvose mapapu neitsvo mbiri. Pakadaro, kana kukanganiswa vari chete chiedza kana chete itsvo, ihosha rinonzi Wegener kuti granulomatosis kukwana.

Wegener kuti granulomatosis chinonyanya nevakawanda vanhu vaduku kana repakati, anenge asina kuonana nevana. Asi, zvakadaro, chirwere anokwanisa kuchinja mumazera ose. Gender nhamba kukunda chirwere ichi anosiyana vanyori siyana.

Zvinokonzera chirwere

The zvinokonzera zvirwere zvakadai, akadai Wegener kuti granulomatosis, nhasi haisi aizvinzwisisa. Nyanzvi dzakawanda dzinofunga kuti mhaka chirwere chingava akabatwa mumiririri, nekuti Wegener kwakaita granulomatosis rinowanzoberekera pashure kubaya, SARS, asingaurayiwi kurapa kana chokupfeka. Asi, zvinosuruvarisa kuti microbial mumiririri achiri asina dzinounzwa, saka chirwere chinogona autoimmune.

Vamwe varwere tinovhiringidza poradenitis uye Wegener kuti granulomatosis. Zvinofanira kunzwisiswa kuti kufanana zviratidzo hurwere maviri akasiyana zvachose nokuti poradenitis unovapo nokuda kwemabhakitiriya utachiona (Chlamydia), ukuwo Wegener kuti granulomatosis chinhu autoimmune chirwere.

Zviratidzo uye chirwere fomu

Wegener kuti granulomatosis anogona kutanga pakarepo, asi anogona mumhino zvishoma nezvishoma. Chiratidzo chokutanga chirwere chinogona kunzi tembiricha subfebrile, zvino kunoderedza kudya. Pashure iyo tembiricha anotanga kumuka, uye chirwere mberi.

Vanhuwo zviratidzo chirwere ichi zvinosanganisira:

- uremu;

- nekuneta;

- kukwidza tembiricha;

- marwadzo majoini;

- kurwadziwa sinus chokutsva.

Mukuwedzera, chirwere chinogona kukanganisa zvikamu zvakasiyana-siyana dzomuviri, zvichipa zviratidzo zvakasiyana zvachose. Somuenzaniso, pamwe kukundwa pamusoro kwokunze kufema runny mhino chete kusingafadzi purulent reropa nokupesana, necrotic nasal mucosa, uyewo nyoro mukanwa uye tonsils.

A generalized chimiro chirwere rinopa mishoma, kwakakomba kuomesa ganda, zvikurukuru, sevanhu ropa, nodular, necrotic okunze, uye mune mamwe mapoka varwere, uye pericarditis, myocarditis kana bronchitis.

chirwere chirwere

Zvikurukuru kuti vanofungidzirwa granulomatosis varwere Wegener vanofanira kupfuura urinalysis kuvapo mapuroteni uye ropa masero matsvuku ari weti. Uyezve X-ray mifananidzo dzinoitwa sinuses uye muchipfuva, Kuti ndione Kumwe kuchinja kunotanga. Uyezve, Kuongororwa ropa achatorwa uye, zvikurukuru, akatsunga nokuda ESR uye C-reactive mapuroteni. Panewo zvimwe kunzwisisa, asi chaizvo kuongorora kuziva antineyrofilnyh cytoplasmic antibodies.

pakurapa chirwere

Wegener kwakaita granulomatosis, pasina kurapwa murwere anogona kutungamirira kurufu mukati maviri mitatu. kurapwa All dzinowanzotsigi- zvainanga iri kudzvinyirira of zvirwere, uyewo vemo anogumbura siyana. Chinonyanya dzakakurumbira zvinodhaka ndivo corticosteroids uye cyclophosphamide. mishonga izvi zvinofanira kutorwa kusvikira kuregererwa chirwere, uye ipapo haana watangazve Hodgkin nechirwere, zvinogona kuwedzerwa navo asi uye methotrexate, izvo zvinofanira kutora vaviri makore.

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