Utano, Zvirwere uye Conditions
The anomaly Arnold Chiari
Anomaly Arnold Chiari akaperekedza dystopia (kukanganisa nzvimbo) zvivako zviri posterior cranial fossa zvaizopedza navo kuburikidza guru dzikapupurira mutsipa kunze dehenya kupinda musana mugero. A kusuduruka cerebellar tonsils kana chikamu kune rokumusoro chikamu vertebral mugero.
Kune mhando ina chirwere ichi. Anomaly Arnold Chiari Type 1 kunoratidzwa zvaizopedza cerebellar tonsils, kwete pamwe okuwedzera anomalies uropi kukura. Izvi mhando kuonekwa vanhu pashure matatu. The mhando chechipiri kutyora nzvimbo zvivako zviri posterior fossa uye cerebellar tonsils. Kakawanda izvi mhando kunokwanisa kuonekwa mune vana. A chechitatu mhando anomaly nzvimbo zvinosanganisira kutyorwa zvinenge zvivako zvose zviri zadnecherepnoy fossa. Kuratidzwa ichi mhando haienderani noupenyu. Wechina mhando anomaly ari nekupedza achinzi kusiyana pamusoro underdevelopment yacho cerebellum. Modern neNeurosurgery akarirondedzera kuna Dandy-Walker syndrome.
In cerebellum indentation chokumusoro chikamu musana Canal ari kuvhiringidza inowanzotorwa water drainage doro kuti inodzivirira uropi uye musana. Abnormalities mu CSF riparadzirwe kunogona kukonzera blockage kuti zvitange anonongedzera kubva uropi kuti nhengo kana kuunganidza cerebrospinal mvura. The kumanikidzwa kuti cerebellum ane pamusoro musana kunogona syringomyelia.
Maererano nenyanzvi dzakawanda, Arnold Chiari anomaly runoonekwa kuva nhaka chirwere. Zvisinei, zvinofanira kucherechedzwa kuti zvidzidzo zvainanga kuferefeta chinhu ichi, vari panguva kutanga danho.
Varwere vakawanda vanorwara chirwere ichi, hazvina kuchengetwa zviratidzo kana zviratidzo. Vanaamai vakadaro vanopiwa hapana kurapwa. Kuonekwa zvirwere rinowanikwa chete mune chirwere vamwe zvirwere.
Kukura chirwere kakawanda achiperekedzwa nemusoro, kushatiriswa vangakosora, sneezing kana mumuviri overexertion, chiveve uye tingling mumaoko, zvaipesana tembiricha-inonyatsoziva uye somugumisiro, kakawanda kutsva. Uyezve, nokuti chirwere hwokuratidza kurwadziwa remuromo kana remuromo nharaunda, kuti nguva nenguva raiiswa pamafudzi. Pane matambudziko kuramba pachiyero (gogonera gait) uye kwakaderera ruoko Kufambisa.
Nokuti vazhinji zviratidzo hosha runowanzotaurwa nezvarwo zvirwere, zvinokosha kuti chirwere zvachose.
Chirwere matanho kutanga kuongorora uye anoshivirira uchibvunzurudzwa. Kana murwere anonyunyuta kurwadziwa mumusoro, asi chikonzero panowanikwa kwavo hakusi pachena unyanzvi munhu, zvichava kupiwa MRI. Diagnostics achibvumira zvakakwana zvakarurama kuziva kuvapo chirwere.
Mune zvimwe zviitiko, Arnold Chiari anomaly anova mberi chirwere inotungamirira dzakakomba zvikuru matambudziko. Izvi zvinosanganisira hydrocephalus (zvakawandisa mvura muuropi). Saka vanotarisira kuti aida kuchinja chubhu nokuda kupomba ari cerebrospinal mvura kune imwe nzvimbo mumuviri. Matambudziko chirwere zvinosanganisirawo dzomuviri. Inokudziridza somugumisiro musana compression. Syringomyelia chokuita kuti zvichibvira matambudziko. Zvinonzi pamwe nokuumbwa cysts iri musana kana mhango, iyo izere cerebrospinal mvura uye anopa basa.
Varwere vane Arnold-Chiari abnormality kurapwa anopiwa zvinoenderana kwokuomerwa mamiriro. Pasina zviratidzo, kazhinji yakatarwa dzose zvichiongororwa uye inspections. Kana kuratidzwa zviratidzo chiremba chikuru anogona mishonga inonyaradza marwadzo omusoro. Zvisinei, vakawanda pakurapa chirwere zvinoitwa surgically.
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